Case Report

Vol. 4 No. 4 (2017): European Journal of Rheumatology
DOI: https://doi.org/10.5152/eurjrheum.2017.17023

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Published: Sep 3, 2019
Keywords:
Asherson's syndrome, catastrophic antiphospholipid syndrome, antiphospholipid syndrome, antiphospholipid antibodies, multiple thromboses

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Flavio Signorelli
Department of Internal Medicine, Hospital Universitário Clementino Fraga Filho, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Brazil; Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro
Gustavo Guimarães Moreira Balbi
Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro, Rio de Janeiro, Brazil
Roger A. Levy
Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro, Rio de Janeiro, Brazil

Catastrophic antiphospholipid syndrome: A case with unusual findings revealed in autopsy and a brief literature update

Main Article Content

Flavio Signorelli
Department of Internal Medicine, Hospital Universitário Clementino Fraga Filho, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Brazil; Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro
Gustavo Guimarães Moreira Balbi
Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro, Rio de Janeiro, Brazil
Roger A. Levy
Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro, Rio de Janeiro, Brazil

Abstract

Abstract


Catastrophic antiphospholipid syndrome (CAPS) is a rare and life-threatening disease. It is characterized by multiple arterial and/or venous thrombotic events, including the microcirculation, occurring in a short period, and can affect any system. Catastrophic antiphospholipid syndrome can occur in individuals with known APS under treatment, or it can be its first manifestation; in most cases, there is a triggering factor that can be identified. In this case report, we report a case of CAPS with multiple thromboses at unusual sites, including the lungs, coronary arteries, stomach, thyroid, gastrocnemius muscles, lymph nodes, and bladder, in a patient with previous diagnosis of systemic lupus erythematosus.





 



 



Cite this article as: Signorelli F, Balbi GGM, Levy RA. Catastrophic antiphospholipid syndrome: A case with unusual findings revealed in autopsy and a brief literature update. Eur J Rheumatol 2017; 4: 281-3.


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