European Journal of Rheumatology
Case Report

Therapy resistant idiopathic scleredema: an underlying pathology not always present

1.

Department of Internal Medicine, Division of Rheumatology, Ege University Faculty of Medicine, İzmir, Turkey

2.

Department of Rheumatology, Koç University Faculty of Medicine, İstanbul, Turkey

Eur J Rheumatol 2015; 2: 163-164
DOI: 10.5152/eurjrheum.2015.0004
Read: 22 Downloads: 2 Published: 03 September 2019

Abstract

Scleredema is a rare connective tissue disorder of unknown pathogenesis. Three types of scleredema have been described, based on its association with postinfection, monoclonal gammopathy and diabetes mellitus. We report herein a case of scleredema which the diagnosis didn’t get specified. The patient was followed regularly for 13 years and did not respond to various combinations of immunosuppressants and psoralen plus ultraviolet A therapy. Treatment of scleredema is quite difficult and of limited success. At present, there is no proved treatment for this disease.

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ISSN2147-9720 EISSN 2148-4279